Page 207 - 2021 IDMT Digital
P. 207

HYPERTROPHIC CARDIOMYOPATHY (HCM)
          Introduction:
            •  +\SHUWURSKLF &DUGLRP\RSDWK\  +&0  LV WKH OHDGLQJ FDXVH RI VXGGHQ GHDWK DPRQJ
               \RXQJ DWKOHWHV
            •  +&0 RFFXUV ZKHQ WKH VHSWXP LV HQODUJHG DORQJ ZLWK HQODUJHPHQW RI WKH /9 WLVVXH
                 o  7KLV FDQ OHDG WR heart DUUK\WKPLDV FDXVLQJ sudden GHDWK
          Subjective:
            •  6LJQV DQG 6\PSWRPV
                 o  )LUVW VLJQ RI +&0 PLJKW EH GHDWK
                 o  6KRUWQHVV RI EUHDWK HVSHFLDOO\ GXULQJ H[HUWLRQ
                 o  &KHVW SDLQ
                       ƒ  6\QFRSDO HSLVRGH SRVW-H[HUWLRQ
            •  )RFXVHG +LVWRU\
                 o  6\QFRSDO HSLVRGHV
                 o  )DPLO\ KLVWRU\ RI VXGGHQ FDUGLDF GHDWK  6&'
                 o  6KRUWQHVV RI EUHDWK RU FKHVW SDLQ HVSHFLDOO\ ZLWK H[HUFLVH
          Objective:
            •  3K\VLFDO ([DP
                 o  %LVferious SXOVH  GRXEOH SXOVH IHOW ZLWK V\VWROLF EHDW DW FDURWLG DUWHU\
                 o  /RXG V\VWROLF PXUPXU WKDW GLVDSSHDUV ZKLOH VTXDWWLQJ DQG JHWV ORXGHU ZKHQ
                    VWDQGLQJ  RXWIORZ REVWUXFWLRQ
            •  7RROV
                 o  (.* may VKRZ OHIW YHQWULFXODU K\SHUWURSK\  /9+  or non-specific abnormalities
          Assessment:
            •  'LIIHUHQWLDO
                 o  0,  (.* ZLOO LQGLFDWH 67 HOHYDWLRQ
                 o  9HQWULFXODU 7DFK\FDUGLD
                 o  9HQWULFXODU )LEULOODWLRQ
                 o  6\QFRSH  SDWLHQW PD\ KDYH KLVWRU\ RI QXPHURXV HSLVRGHV
                 o  +HDUW IDLOXUH  DGYHQWLWLRXV VRXQGV SHULSKHUDO HGHPD ZLOO EH SUHVHQW
          Plan:
            •  3UHSDUH IRU $&/6 LQWHUYHQWLRQ
            •  ,I VXVSLFLRXV 3( (.* ILQGLQJV  FRQWDFW pUHFHSWRU
                 o  &RQVLGHU LPPHGLDWH HYDFXDWLRQ IRU FDUGLRORJ\ HYDOXDWLRQ
            •  $YRLG H[HUWLRQDO DFWLYLWLHV XQWLO FOHDUHG E\ FDUGLRORJ\
            •  &RQVLGHU VFUHHQLQJ WDFWLFDO DWKOHWHV



















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